Synonyms

Benign peripheral nerve sheath tumour with heterologous differentiation

Category

Soft tissue

Behaviour

Benign

Gender

Both equally

Tissue of Origin

Neural

Epidemiology

• Benign nerve sheath tumour with skeletal muscle differentiation
• Rare

Clinical Features

Firm mass along nerve

Location

Any soft tissue site near nerves

Imaging

MRI: well-defined mass

Pathology

• Nerve sheath tumour with skeletal muscle differentiation
• Benign spindle cells and myogenic component

Genetics

Sporadic

Treatment

Surgical excision

Prognosis

Excellent - Benign

Key Points

Benign nerve sheath tumour variant

Workup - Blood Tests

No blood tests required

Workup - Local Imaging

MRI for assessment

Workup - Biopsy

Confirm diagnosis

Workup - Staging

No staging required