Synonyms

• Osteofibrous dysplasia proper
• congenital fibrous defect of tibia and fibula

Category

Bone

Behaviour

Benign

Grade

Low

Gender

Both equally

Tissue of Origin

Bone

Epidemiology

• Benign lesion of tibia and fibula
• Presents in children and adolescents
• Progressive during growth years

Clinical Features

• Anterior tibial bowing
• Mass palpable on anterior tibia
• Pathological fracture possible

Location

• Anterior tibia
• Fibula
• Bilateral in 10%

Imaging

• Plain radiograph: lytic lesion with mixed sclerosis, anterior tibial bowing
• MRI: well-defined lesion in cortex

Pathology

• Fibrous tissue with scattered osteoid formation
• Benign fibroblasts and osteoblasts
• No significant atypia

Genetics

Sporadic occurrence

Treatment

• Observation - regresses with skeletal maturity
• Curettage if fracture or significant deformity

Prognosis

Excellent - typically regresses after skeletal maturity

Key Points

• Benign congenital Fibrous lesion
• Anterior tibial bowing is characteristic
• Resolves with skeletal maturity

Workup - Blood Tests

No blood tests required

Workup - Local Imaging

• Plain radiograph - characteristic anterior bowing
• MRI if diagnostic uncertainty

Workup - Biopsy

Biopsy rarely required

Workup - Staging

No staging required